Treated Rosai-Dorfman Disease: An Unusual Cause of Biliary Obstruction A CASE TO REMEMBER
نویسندگان
چکیده
R osai-Dorfman disease, also known as sinus histiocytosis with massive lymphadenopathy (SHML), is a rare idiopathic disorder of histiocytic proliferation. According to a review of the entity by Foucar et al (1), the typical patient profile is a 20year-old white or black male who presents with painless bilateral cervical lymphadenopathy. The clinical course is variable ranging from self-limited and indolent with spontaneous regression to, less commonly, aggressive and fulminant. A large number of patients
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Rosai-Dorfman Disease: A Case Report and Literature Review
Rosai-Dorfman disease or sinus histiocytosis with massive lymphadenopathy is a rare disorder that typically manifests as lymphadenopathy and systemic symptoms whose etiology remains poorly elucidated. The diagnosis is based on immunohistochemistry. Its treatment is poorly defined but the prognosis is usually favorable. Here we report a 14 year old boy who presented with massive bilateral cervi...
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